One case of congenital no cervix, no vaginal, bilateral chocolate cysts with MRKH syndrome (type II)

Corresponding author: WANG LieHong, doctorwifi@126.com

DOI: 10.12201/bmr.202501.00072

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  Abstract: In the clinical work of obstetrics and gynecology,congenital absence of cervix,absence of vagina,bilateral chocolate cyst with MRKH syndrome (type II) is an extremely rare congenital dysmorphic disease of the reproductive system,which is typically manifested by dysplasia or absence of uterus and vagina.Patients with MRKH syndrome type II often have ovarian lesions (eg,bilateral chocolate cysts) and other systemic abnormalities (eg,urinary or skeletal dysplasia) in addition to genital tract abnormalities.This article describes the treatment of a patient with congenital cervical,nonvaginal,bilateral chocolate cyst and MRKH syndrome (type II).The patient,a 17-year-old female,was admitted to the hospital complaining of menstrual cramps and lower abdominal pain for 2 days.Gynecologic examination reveals vulva:poorly developed pubic hair,poorly developed labia minora,small hymen orifice,visible separation in the middle,and cotton swabs unable to penetrate.Pelvic MRI was performed immediately afterwards,and the results showed endometrial thickening,cervical dysplasia,no visible in the lower one-third of the vagina,and no development of the caudal vertebrae.Combined with the results of the patients auxiliary examination, under the discussion of the department director and all doctors,and with the consent of the patients family,it is planned to decide to undergo laparoscopic vaginoplasty (acellular allodermis) + cervicopy + hysteroscopy + laparoscopic bilateral ovarian cystectomy + ultrasound-guided uterine balloon placement.After careful care after the operation,the results of the re-examination of B-ultrasound improved significantly,and the patient was successfully discharged from the hospital.

  Key words: MRKH syndrome; chocolate cyst; congenital malformation of the female genital tract; vaginoplasty.

  Submit time: 23 January 2025

  Copyright: The copyright holder for this preprint is the author/funder, who has granted biomedRxiv a license to display the preprint in perpetuity.
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